Information about formulas is provided for reference only. Consult physicians, registered dietitians (nutritionists), or other medical professionals about dietary matters.

Products

• GA – GA is a lysine- and tryptophan-free, iron-fortified dietary powder for infants, children and adults with glutaric acidemia type I
• LMD – LMD is a leucine-free, iron-fortified dietary powder for infants, children and adults with disorders of leucine metabolism. LMD stands for leucine metabolism disorders.
• OA 1 – OA 1 is an isoleucine-, methionine-, threonine- and valine-free, iron-fortified dietary powder for infants and toddlers with propionic acidemia or methylmalonic acidemia. OA stands for organic acid.
• OA 2 – OA 2 is an isoleucine-, methionine-, threonine- and valine-free dietary powder for the dietary management of children and adults with propionic acidemia or methylmalonic acidemia. OA stands for organic acid.
• PFD 1 – PFD 1 is a protein- and amino acid-free product* designed with vitamins and minerals as well as the essential fatty acids for infants and toddlers with various amino acid metabolic disorders.
• PFD 2 – PFD 2 is a protein-free and amino acid-free product designed to help meet the calorie, vitamin, mineral, and essential fatty acid needs of children and adults with amino acid metabolic disorders. PFD 2 can be mixed with condition-specific amino acids or protein to make a nutritionally complete beverage or used as a calorie, vitamin and mineral supplement in cases where amino acid and protein requirements are met but needs for calories, vitamins, and minerals are not.

Formula coverage assistance for Nutricia Metabolic Formulas
nutricia-na.com/nutricianavigator/   

Products

• GA1 Anamix Early Years – for infants with Glutaric Acidemia, Type 1
• GA1 Next – for 8 years to adult for use in Glutaric Acidemia Type 1
• GlutarAde Essential GA-1 
• GlutarAde GA1 Amino Acid Blend
• GlutarAde GA1 Junior
• IVA Anamix Early Years – for infants with Isovaleric Acidemia
• IVA Anamix Next – for 8 years to adult for use in Isovaleric Acidemia
• XLEU Maxamum – 8 years to adult for use in Isovaleric Acidemia
• MMA/PA Anamix Early Years – infants with MMA/PA
• MMA.PA Anamix Next – for 8 years to adult for use in MMA/PA
• XMTVI Maxamum – 8 years to adult for use in Propionic and Methylmalonic Acidemias

Products

• Propimex-1 – infants and toddlers with Propionic and Methylmalonic acidemias
• Propimex-2 – children and adults with Propionic and Methylmalonic acidemias
• I-Valex-1 – infants and toddlers with Isovaleric Acidemia, 3-Hydroxy-3-methylglutaric aciduria*, 3-Methylcrotonylglycinuria, 3-Methylglutaconic aciduria*
• I-Valex-2 – children and adults with Isovaleric Acidemia, 3-Hydroxy-3-methylglutaric aciduria, 3-Methylcrotonylglycinuria, 3-Methylglutaconic aciduria*
• Glutarex-1 – infants and toddlers with Glutaric Acidemia, Type 1
• Glutarix-2 – children and adults with Glutaric Acidemia, Type 1
• Ketonex® – 1 – Beta-ketothiolase deficiency3-Hydroxyisobutyric aciduria
• Ketonex® – 2 – Beta-ketothiolase deficiency3-Hydroxyisobutyric aciduria
• Pro-Phree – Protein Free Diet Powder for use with any of these disorders.